Aplasia cutis congenita is a congenital disorder seen in newborns. It typically manifests as an absence of the skin of the scalp but can occur in any location. While most children have no other associated abnormalities, cleft lip and palate, tracheoesophageal fistula, double cervix and uterus, patent ductus arteriosus, coarctation of the aorta, cutis marmorata telangiectatica congenita, arteriovenous (AV) fistulas, central nervous system (CNS) dysraphisms, and intestinal lymphangiectasia have been reported with the anomaly. The newborn can present with an open erosion or a healed, depressed scar.