Contents

SynopsisCodesBest TestsReferences
Evans syndrome
Other Resources UpToDate PubMed

Evans syndrome

Other Resources UpToDate PubMed

Synopsis

A rare, idiopathic autoimmune hemolytic disorder of unknown etiology, identified by its characteristic features of autoimmune hemolytic anemia (AIHA), immune thrombocytopenia (simultaneously or sequentially), and sometimes neutropenia. Dysfunction of the autoimmune system causes antibodies to attack the body's red blood cells (AIHA) and platelets (immune thrombocytopenia) in relapsing episodes. Onset may be in childhood (acute) or adulthood (chronic). Physical exam may identify signs and symptoms of fatigue, dyspnea, pallor, petechiae, and presyncope. Complications may include severe bleeding and increased risk of death.

Treatment is often not warranted, but depending on the severity of the disorder, can include corticosteroids and other prescription drugs, spleen removal, and in severe cases, platelet transfusion.

Codes

ICD10CM:
D69.41 – Evans syndrome

SNOMEDCT:
75331009 – Evans syndrome

Best Tests

Subscription Required

References

Subscription Required

Last Updated:01/12/2016
Copyright © 2024 VisualDx®. All rights reserved.
Evans syndrome
Print  
A medical illustration showing key findings of Evans syndrome : Fatigue, Hemolytic anemia, Dyspnea, Pallor, Presyncope, WBC decreased, PLT decreased
Copyright © 2024 VisualDx®. All rights reserved.