Angiokeratoma circumscriptum in Adult
Alerts and Notices
Important News & Links
Synopsis
Angiokeratoma circumscriptum is a benign, relatively uncommon form of cutaneous vascular ectasia. It presents as one or more dark red, maroon, or blue-black papule, plaque, or nodule that may have a keratotic or verrucous surface. It is most often found unilaterally on a lower limb.
Angiokeratoma circumscriptum has been associated with Klippel-Trenaunay-Weber syndrome (osteohypertrophy of a limb), Cobb syndrome, port-wine stain, cavernous hemangiomas, and arteriovenous fistulas. The condition is present at birth or develops by early childhood, with lesions often increasing in size during adolescence. Female patients are affected more commonly than male patients.
Angiokeratoma circumscriptum has been associated with Klippel-Trenaunay-Weber syndrome (osteohypertrophy of a limb), Cobb syndrome, port-wine stain, cavernous hemangiomas, and arteriovenous fistulas. The condition is present at birth or develops by early childhood, with lesions often increasing in size during adolescence. Female patients are affected more commonly than male patients.
Codes
ICD10CM:
D23.9 – Other benign neoplasm of skin, unspecified
SNOMEDCT:
21848000 – Angiokeratoma circumscriptum
D23.9 – Other benign neoplasm of skin, unspecified
SNOMEDCT:
21848000 – Angiokeratoma circumscriptum
Look For
Subscription Required
Diagnostic Pearls
Subscription Required
Differential Diagnosis & Pitfalls
To perform a comparison, select diagnoses from the classic differential
Subscription Required
Best Tests
Subscription Required
Management Pearls
Subscription Required
Therapy
Subscription Required
References
Subscription Required
Last Reviewed:10/04/2021
Last Updated:10/04/2021
Last Updated:10/04/2021