Pemphigus vulgaris in Child
See also in: Anogenital,Oral Mucosal LesionAlerts and Notices
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Synopsis
PV typically affects adults, with a mean age of onset in the fifth and sixth decades of life. Variants of the ST18 gene have been found to confer increased risk of PV in some populations.
Childhood PV, which refers to disease in children younger than 12 years, and juvenile PV, which refers to disease in adolescents aged 13-18 years, are rare, comprising less than 5% of all cases. The mucocutaneous type is more frequently observed in children and adolescents.
PV is characterized by painful erosions on the oral mucosa and flaccid bullae and erosions on the skin. Severe cases of PV can be life-threatening, and complications can be related to immunosuppression from drugs used to treat severe PV, secondary infections, loss of the skin barrier, and poor oral intake.
Codes
L10.0 – Pemphigus vulgaris
SNOMEDCT:
49420001 – Pemphigus vulgaris
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Last Updated:01/10/2022
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