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Retroperitoneal cystic lymphangioma
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Retroperitoneal cystic lymphangioma

Contributors: Michael W. Winter MD, Paritosh Prasad MD
Other Resources UpToDate PubMed

Synopsis

Lymphangiomas are rare benign cystic tumors caused by uncontrolled lymphatic growth. Most lymphangiomas arise in the axilla or neck. In approximately 1% of cases, lymphangiomas develop in the retroperitoneal space, characterized as a retroperitoneal cystic lymphangioma.

These tumors can be asymptomatic, but often, due to their size and location, patients will present with a palpable abdominal mass, bowel obstruction, abdominal pain, anorexia, weight loss, ascites, or obstructive nephropathy from ureter compression. Asymptomatic cases can be found incidentally during surgery or autopsy.

The diagnosis of a cystic lymphangioma typically requires pathology, as the appearance of a complex cyst on cross-sectional imaging is not specific to these types of tumors.

Codes

ICD10CM:
D18.1 – Lymphangioma, any site

SNOMEDCT:
40225001 – Cystic lymphangioma

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Diagnostic Pearls

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Differential Diagnosis & Pitfalls

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Best Tests

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Management Pearls

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Therapy

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References

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Last Reviewed:03/06/2018
Last Updated:03/06/2018
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Retroperitoneal cystic lymphangioma
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A medical illustration showing key findings of Retroperitoneal cystic lymphangioma : Diarrhea, Fever, Nausea, Abdominal distension, Epigastric pain, Anorexia, LUQ pain, Palpable abdominal mass
Copyright © 2024 VisualDx®. All rights reserved.